Fibrodysplasia Ossificans Progressiva is a rare illness of the connective tissue, characterized by bilateral congenital malformations of the big toe and progressive ossifications of soft tissue that produces permanent immobilizations of the joints. We present a case of a 21 years old feminine patient that came with pain and inflammation history on right lower limb, as an illness complication that the patient refers began since childhood. She recounts that when she was two years old, a painful and indurate mass appeared in left cervical region. A biopsy of the mass was performed, from this moment she presented major constraint to mobilize left upper limb and left cervical region. At age of twelve myositis ossiicans diagnosis was confirmed. At physical examination we detected in big toes, microdactilia. The left arm had restricted abduction and left hemitorax was rigid and with scoliosis.
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