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The Sturge-Weber syndrome is a rare congenital syndrome with a low incidence in children. Usually, it shows as a nevus flammeus with a typical distribution of the ophthalmic branch of the trigeminal nerve, along with leptomeningeal angiomatosis and glaucoma. We may add to this calcinosis in the occipital and frontoparietal regions, seizures, headaches, transient neurological stroke-like episodes, and progressive cognitive impairment.
We present the case of a 59-year-old male who went to the emergency department with a history of a convulsive event followed by coffee ground vomiting. During his hospitalization, a brain tomography was performed, which showed intracerebral calcinosis. Along with the findings of the physical examination, this led to the diagnosis of Sturge-Weber syndrome.